EXTENDED REPORT Disease progression in systemic sclerosis-overlap syndrome is significantly different from limited and diffuse cutaneous systemic sclerosis
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چکیده
Disease progression in systemic sclerosis-overlap syndrome is significantly different from limited and diffuse cutaneous systemic sclerosis Pia Moinzadeh, Elisabeth Aberer, Keihan Ahmadi-Simab, Norbert Blank, Joerg H W Distler, Gerhard Fierlbeck, Ekkehard Genth, Claudia Guenther, Ruediger Hein, Joerg Henes, Lena Herich, Ilka Herrgott, Ina Koetter, Alexander Kreuter, Thomas Krieg, Kathrin Kuhr, Hanns-Martin Lorenz, Florian Meier, Inga Melchers, Hartwig Mensing, Ulf Mueller-Ladner, Christiane Pfeiffer, Gabriela Riemekasten, Miklós Sárdy, Marc Schmalzing, Cord Sunderkoetter, Laura Susok, Ingo H Tarner, Peter Vaith, Margitta Worm, Gottfried Wozel, Gabriele Zeidler, Nicolas Hunzelmann, and all participating DNSS centers
منابع مشابه
بررسی علایم بالینی بیماران مبتلا به اسکلرودرمی نوع محدود و منتشر پوستی در سه سال اولیه شروع بیماری و مقایسه آن با شش سال پس از شروع اسکلرودرمی
Systemic sclerosis is a generalized disorder of connective tissue, in which the pattern of disease extent, progression and outcome is heterogenous. To determine clinical features, disease extent and progression, we studied our patients in two phases of disease early (the first 3 years) and late phases (after 6 years of disease). 19 patients had diffuse cutaneous and 34 patients had limited cuta...
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Background: Systemic sclerosis is an autoimmune connective tissue disorder which is characterised by cutaneous and internal organ fibrosis. Raynaud’s phenomenon is the earliest feature and may precede the onset of the disease by months to years. The heart, lungs, gastrointestinal tract, kidneys and other organs may be involved. Our aim was to evaluate skin thickness and echogenicity in systemic...
متن کاملDisease progression in systemic sclerosis-overlap syndrome is significantly different from limited and diffuse cutaneous systemic sclerosis
BACKGROUND Systemic sclerosis (SSc)-overlap syndromes are a very heterogeneous and remarkable subgroup of SSc-patients, who present at least two connective tissue diseases (CTD) at the same time, usually with a specific autoantibody status. OBJECTIVES To determine whether patients, classified as overlap syndromes, show a disease course different from patients with limited SSc (lcSSc) or diffu...
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806 Ann Dermatol Received March 16, 2016, Revised November 3, 2016, Accepted for publication November 7, 2016 Corresponding author: Hei Sung Kim, Department of Dermatology, Incheon St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, 56 Dongsu-ro, Bupyeong-gu, Incheon 21431, Korea. Tel: 82-32-280-5700, Fax: 82-32-506-9514, E-mail: [email protected] This is an Open Ac...
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